PDF | On Apr 1, , SANTIAGO MUZZO PONS and others published Enfermedad de hand Schuller Christian. Purpose/Material and Method: To describe the clinical case of a month-old boy with Hand-Schuller-Christian disease. Exophthalmos was the only systemic. Diabetes insipidus and growth retardation are common manifestations of hypothalamic involvement in patients with Hand-Schuller-Christian disease ( HSCD).

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Symptoms Signs Labs Diagnosis Extra: Related Bing Images Extra: Diagnosis Skin biopsy Bone Marrow Biopsy. Related links to external sites from Bing. Langerhans-cell granulomatosis can involve a single organ, or can be a systemic disorder.

Langerhans cell histiocytosis may also affect the pituitary gland which makes hormones that control other glands and many body functions, especially growth.

Langerhans cell histiocytosis is most common in children and young adults. Definition NCI A neoplastic proliferation of Langerhans cells which contain Birbeck granules by ultrastructural examination. Three major overlapping syndromes are recognized: The clinical course is generally related to the number of organs affected at presentation.

Langerhans cell histiocytosis in the maxillofacial area in adults: Report of three cases

There is involvement of wchuller sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. Definition CSP group of disorders of histiocyte proliferation which includes Letterer-Siwe disease; Hand-Schueller-Christian syndrome; and eosinophilic granuloma; Langerhans cells are components of the lesions.


Related Topics in Histiocytosis. Hematology and Oncology Chapters.

Hand-Schuller-Christian Syndrome

Hematology and Oncology – Histiocytosis Pages. Back Links pages that link to this page. Search other sites for ‘Hand-Schuller-Christian Syndrome’. A group of rare disorders in which too many Langerhans cells a type of white blood cell grow in certain tissues and organs including the bones, skin, and lungs, and damage them.

A neoplastic proliferation of Langerhans cells which contain Birbeck granules by ultrastructural examination. A multifocal, unisystem form of Langerhans-cell histiocytosis.